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visceral heterotaxy

MONDO:0018677

Also known as: heterotaxia, heterotaxia syndrome, heterotaxy syndrome, heterotaxy, visceral, incomplete situs inversus

MONDO:
MONDO:0018677
Orphanet:
157769
Rare disease35 associated genes

Description

A rare, genetic disorder in which symptoms are generally secondary to the abnormal location of the organs within the thoracic, abdominal, or peritoneal cavities. Anatomic and functional problems can include cardiac defects, intestinal malrotation leading to volvulus, biliary atresia, and various defects of the central nervous system, urinary tract, and skeleton.

Associated genes

+25 more genes — install the extension to see the full list inline on any page.

External references

Sources: MONDO (CC BY 4.0), Open Targets (CC0), Orphanet (CC BY 4.0).

Not for sole clinical decision-making. Always verify against primary sources.