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Usher syndrome type 1

MONDO:0010168

Also known as: USH1, Usher syndrome type 1, Usher syndrome, type 1, retinitis pigmentosa and congenital deafness, USH1A

MONDO:
MONDO:0010168
Orphanet:
231169
Rare disease91 associated genes

Description

A syndrome characterized by congenital, bilateral, severe sensorineural hearing loss, abnormalities in the vestibular system, and adolescent-onset retinitis pigmentosa.

Associated genes

+81 more genes — install the extension to see the full list inline on any page.

External references

Sources: MONDO (CC BY 4.0), Open Targets (CC0), Orphanet (CC BY 4.0).

Not for sole clinical decision-making. Always verify against primary sources.