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Joubert syndrome

MONDO:0018772

Also known as: CPD IV, Joubert syndrome, Joubert syndrome type A, Joubert-Boltshauser syndrome, cerebelloparenchymal disorder IV

MONDO:
MONDO:0018772
Orphanet:
475
Rare disease57 associated genes

Description

Joubert syndrome (JS) is characterized by congenital malformation of the brainstem and agenesis or hypoplasia of the cerebellar vermis leading to an abnormal respiratory pattern, nystagmus, hypotonia, ataxia, and delay in achieving motor milestones.

Associated genes

+47 more genes — install the extension to see the full list inline on any page.

External references

Sources: MONDO (CC BY 4.0), Open Targets (CC0), Orphanet (CC BY 4.0).

Not for sole clinical decision-making. Always verify against primary sources.