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left ventricular noncompaction

MONDO:0018901

Also known as: LVNC, Lv non-compaction syndrome, left ventricular hypertrabeculation, left ventricular non-compaction cardiomyopathy, left ventricular non-compaction syndrome

MONDO:
MONDO:0018901
Orphanet:
54260
Rare disease58 associated genes

Description

Left ventricular noncompaction (LVNC) is a rare cardiomyopathy characterized anatomically by prominent left ventricular trabeculae and deep intratrabecular recesses causing progressive systolic and diastolic dysfunction, conduction abnormalities, and occasionally thromboembolic events.

Associated genes

+48 more genes — install the extension to see the full list inline on any page.

External references

Sources: MONDO (CC BY 4.0), Open Targets (CC0), Orphanet (CC BY 4.0).

Not for sole clinical decision-making. Always verify against primary sources.