catecholaminergic polymorphic ventricular tachycardia
MONDO:0017990Also known as: CPVT, bidirectional tachycardia induced by catecholamine, catecholaminergic polymorphic ventricular tachycardia, double tachycardia induced by catecholamines, malignant paroxysmal ventricular tachycardia
- MONDO:
- MONDO:0017990
- Orphanet:
- 3286 ↗
Rare disease42 associated genes
Description
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic disorder characterized by adrenergically induced ventricular tachycardia (VT) manifesting as syncope and sudden death.
Associated genes
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